Computed tomography after lymphangiography in the diagnosis of intestinal lymphangiectasia with protein-losing enteropathy in Noonan's syndrome.
Identifieur interne : 00A270 ( Main/Exploration ); précédent : 00A269; suivant : 00A271Computed tomography after lymphangiography in the diagnosis of intestinal lymphangiectasia with protein-losing enteropathy in Noonan's syndrome.
Auteurs : M. Keberle [Allemagne] ; H. Mörk ; M. Jenett ; D. Hahn ; M. ScheurlenSource :
- European radiology [ 0938-7994 ] ; 2000.
Descripteurs français
- KwdFr :
- Adulte, Diagnostic différentiel, Entéropathie exsudative (imagerie diagnostique), Entéropathie exsudative (étiologie), Humains, Lymphangiectasie intestinale (), Lymphangiectasie intestinale (imagerie diagnostique), Lymphographie, Mâle, Syndrome de Noonan (), Syndrome de Noonan (imagerie diagnostique), Tomodensitométrie.
- MESH :
- imagerie diagnostique : Entéropathie exsudative, Lymphangiectasie intestinale, Syndrome de Noonan.
- étiologie : Entéropathie exsudative.
- Adulte, Diagnostic différentiel, Humains, Lymphangiectasie intestinale, Lymphographie, Mâle, Syndrome de Noonan, Tomodensitométrie.
English descriptors
- KwdEn :
- Adult, Diagnosis, Differential, Humans, Lymphangiectasis, Intestinal (complications), Lymphangiectasis, Intestinal (diagnostic imaging), Lymphography, Male, Noonan Syndrome (complications), Noonan Syndrome (diagnostic imaging), Protein-Losing Enteropathies (diagnostic imaging), Protein-Losing Enteropathies (etiology), Tomography, X-Ray Computed.
- MESH :
- complications : Lymphangiectasis, Intestinal, Noonan Syndrome.
- diagnostic imaging : Lymphangiectasis, Intestinal, Noonan Syndrome, Protein-Losing Enteropathies.
- etiology : Protein-Losing Enteropathies.
- Adult, Diagnosis, Differential, Humans, Lymphography, Male, Tomography, X-Ray Computed.
Abstract
Noonan's syndrome is a rare congenital disorder that may be associated with abnormalities in the lymphatic drainage. In this case of a 21-year-old man CT after bipedal lymphangiography confirmed the diagnosis of intestinal lymphangiectasy causing protein-losing enteropathy in Noonan's syndrome by showing contrast-enhanced abnormal lymphatic vessels in the mesentery and the intestinal wall. Because of the benefit of diet in case of intestinal involvement, we recommend a thorough documentation of the lymphatic drainage with lymphangiography followed by CT, if clinical signs of lymphatic dysplasia, such as pleural effusions, lymphedema, or hypoproteinemia are present.
DOI: 10.1007/s003300000384
PubMed: 11044930
Affiliations:
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Keberle</name><affiliation wicri:level="4"><nlm:affiliation>Department of Radiology, Universität Würzburg, Germany.</nlm:affiliation><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Radiology, Universität Würzburg</wicri:regionArea><placeName><settlement type="city">Wurtzbourg</settlement><region type="land" nuts="1">Bavière</region><region type="district" nuts="2">District de Basse-Franconie</region></placeName><orgName type="university">Université de Wurtzbourg</orgName></affiliation></author><author><name sortKey="Mork, H" sort="Mork, H" uniqKey="Mork H" first="H" last="Mörk">H. Mörk</name></author><author><name sortKey="Jenett, M" sort="Jenett, M" uniqKey="Jenett M" first="M" last="Jenett">M. Jenett</name></author><author><name sortKey="Hahn, D" sort="Hahn, D" uniqKey="Hahn D" first="D" last="Hahn">D. Hahn</name></author><author><name sortKey="Scheurlen, M" sort="Scheurlen, M" uniqKey="Scheurlen M" first="M" last="Scheurlen">M. Scheurlen</name></author></analytic><series><title level="j">European radiology</title><idno type="ISSN">0938-7994</idno><imprint><date when="2000" type="published">2000</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term><term>Diagnosis, Differential</term><term>Humans</term><term>Lymphangiectasis, Intestinal (complications)</term><term>Lymphangiectasis, Intestinal (diagnostic imaging)</term><term>Lymphography</term><term>Male</term><term>Noonan Syndrome (complications)</term><term>Noonan Syndrome (diagnostic imaging)</term><term>Protein-Losing Enteropathies (diagnostic imaging)</term><term>Protein-Losing Enteropathies (etiology)</term><term>Tomography, X-Ray Computed</term></keywords><keywords scheme="KwdFr" xml:lang="fr"><term>Adulte</term><term>Diagnostic différentiel</term><term>Entéropathie exsudative (imagerie diagnostique)</term><term>Entéropathie exsudative (étiologie)</term><term>Humains</term><term>Lymphangiectasie intestinale ()</term><term>Lymphangiectasie intestinale (imagerie diagnostique)</term><term>Lymphographie</term><term>Mâle</term><term>Syndrome de Noonan ()</term><term>Syndrome de Noonan (imagerie diagnostique)</term><term>Tomodensitométrie</term></keywords><keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphangiectasis, Intestinal</term><term>Noonan Syndrome</term></keywords><keywords scheme="MESH" qualifier="diagnostic imaging" xml:lang="en"><term>Lymphangiectasis, Intestinal</term><term>Noonan Syndrome</term><term>Protein-Losing Enteropathies</term></keywords><keywords scheme="MESH" qualifier="etiology" xml:lang="en"><term>Protein-Losing Enteropathies</term></keywords><keywords scheme="MESH" qualifier="imagerie diagnostique" xml:lang="fr"><term>Entéropathie exsudative</term><term>Lymphangiectasie intestinale</term><term>Syndrome de Noonan</term></keywords><keywords scheme="MESH" qualifier="étiologie" xml:lang="fr"><term>Entéropathie exsudative</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Adult</term><term>Diagnosis, Differential</term><term>Humans</term><term>Lymphography</term><term>Male</term><term>Tomography, X-Ray Computed</term></keywords><keywords scheme="MESH" xml:lang="fr"><term>Adulte</term><term>Diagnostic différentiel</term><term>Humains</term><term>Lymphangiectasie intestinale</term><term>Lymphographie</term><term>Mâle</term><term>Syndrome de Noonan</term><term>Tomodensitométrie</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Noonan's syndrome is a rare congenital disorder that may be associated with abnormalities in the lymphatic drainage. In this case of a 21-year-old man CT after bipedal lymphangiography confirmed the diagnosis of intestinal lymphangiectasy causing protein-losing enteropathy in Noonan's syndrome by showing contrast-enhanced abnormal lymphatic vessels in the mesentery and the intestinal wall. Because of the benefit of diet in case of intestinal involvement, we recommend a thorough documentation of the lymphatic drainage with lymphangiography followed by CT, if clinical signs of lymphatic dysplasia, such as pleural effusions, lymphedema, or hypoproteinemia are present.</div></front></TEI><affiliations><list><country><li>Allemagne</li></country><region><li>Bavière</li><li>District de Basse-Franconie</li></region><settlement><li>Wurtzbourg</li></settlement><orgName><li>Université de Wurtzbourg</li></orgName></list><tree><noCountry><name sortKey="Hahn, D" sort="Hahn, D" uniqKey="Hahn D" first="D" last="Hahn">D. Hahn</name><name sortKey="Jenett, M" sort="Jenett, M" uniqKey="Jenett M" first="M" last="Jenett">M. Jenett</name><name sortKey="Mork, H" sort="Mork, H" uniqKey="Mork H" first="H" last="Mörk">H. Mörk</name><name sortKey="Scheurlen, M" sort="Scheurlen, M" uniqKey="Scheurlen M" first="M" last="Scheurlen">M. Scheurlen</name></noCountry><country name="Allemagne"><region name="Bavière"><name sortKey="Keberle, M" sort="Keberle, M" uniqKey="Keberle M" first="M" last="Keberle">M. Keberle</name></region></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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